European Journal of Radiology Extra
Volume 79, Issue 2 , Pages e69-e71, August 2011

Ebstein anomaly and double orifice mitral valve–An unusual association

  • Rahul D. Renapurkar

      Affiliations

    • Cardiovascular Imaging Laboratory, Imaging Institute, Cleveland Clinic, Cleveland, OH, United States
    • Corresponding Author InformationCorresponding author at: Thoracic Imaging, Hb6, Imaging Institute, Cleveland Clinic, OH, United States. Tel.: +1 216 445 0582; fax: +1 216 636 0822.
  • ,
  • Ruvin S. Gabriel

      Affiliations

    • Cardiovascular Imaging Laboratory, Imaging Institute, Cleveland Clinic, Cleveland, OH, United States
    • Cardiovascular Imaging Laboratory, Heart and Vascular Institute, Cleveland Clinic, Cleveland, OH, United States
  • ,
  • Allan Klein

      Affiliations

    • Cardiovascular Imaging Laboratory, Heart and Vascular Institute, Cleveland Clinic, Cleveland, OH, United States
  • ,
  • Paul Schoenhagen

      Affiliations

    • Cardiovascular Imaging Laboratory, Imaging Institute, Cleveland Clinic, Cleveland, OH, United States
    • Cardiovascular Imaging Laboratory, Heart and Vascular Institute, Cleveland Clinic, Cleveland, OH, United States
  • ,
  • Janine Arruda

      Affiliations

    • Cardiovascular Imaging Laboratory, Imaging Institute, Cleveland Clinic, Cleveland, OH, United States
    • Cardiovascular Imaging Laboratory, Pediatric Institute, Cleveland Clinic, Cleveland, OH, United States

Received 3 February 2011; received in revised form 3 June 2011; accepted 3 June 2011. published online 29 June 2011.

Highlights

► We report an unusual association between Ebstein anomaly and double orifice mitral valve. ► Echocardiography can demonstrate the two separate orifices in double orifice mitral valve. ► Cardiac MRI can also be used to provide anatomic and functional diagnosis of double orifice mitral valve.

Abstract 

We report an unusual association between Ebstein anomaly of the tricuspid valve and a stenotic double orifice mitral valve diagnosed later in life.

Keywords: Ebstein anomaly, Double orifice mitral valve

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PII: S1571-4675(11)00069-1

doi:10.1016/j.ejrex.2011.06.001

European Journal of Radiology Extra
Volume 79, Issue 2 , Pages e69-e71, August 2011